CARDIOVASCULAR MAGNETIC RESONANCE IN THE EVALUATION OF FIBROFATTY INFILTRATION FOR ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA/CARDIOMYOPATHY (ARVD/C)
نویسندگان
چکیده
منابع مشابه
Arrhythmogenic right ventricular cardiomyopathy mimics: role of cardiovascular magnetic resonance
BACKGROUND Cardiovascular magnetic resonance (CMR) is commonly used in patients with suspected arrhythmogenic right ventricular cardiomyopathy (ARVC) based on ECG, echocardiogram and Holter. However, various diseases may present with clinical characteristics resembling ARVC causing diagnostic dilemmas. The aim of this study was to explore the role of CMR in the differential diagnosis of patient...
متن کاملArrhythmogenic right ventricular cardiomyopathy (ARVC): cardiovascular magnetic resonance update
Arrhythmogenic Right Ventricular Cardiomyopathy (ARVC) is one of the most arrhythmogenic forms of inherited cardiomyopathy and a frequent cause of sudden death in the young. Affected individuals typically present between the second and fourth decade of life with arrhythmias coming from the right ventricle. Pathogenic mutations in genes encoding the cardiac desmosome can be found in approximatel...
متن کاملClinical impact of cardiovascular magnetic resonance in evaluation for possible arrhythmogenic right ventricular dysplasia/cardiomyopathy
Methods Patients referred for assessment of ARVD/C were evaluated. Using 2010 ARVD/C Task Force criteria, clinical history, family history, ECG and other test results were evaluated with and without CMR findings to determine definite, borderline or possible ARVD/C. CMR included assessment of right ventricular(RV) size, function, and regional wall motion(RWM). For alternative diagnoses, tissue c...
متن کاملThe Role of Cardiac Magnetic Resonance Imaging in the Evaluation of Arrhythmogenic Right Ventricular Dysplasia
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a cardiac muscle disorder characterized pathologically by fibrofatty replacement of the right ventricular (RV) myocardium [1]. In the early stage of the disease, structural changes may be confined to, the so called "triangle of dysplasia" in the RV. Clinical expression ranges from an asymptomatic phenotype, arrhythmias or eve...
متن کاملRole of cardiovascular magnetic resonance imaging in arrhythmogenic right ventricular dysplasia
Arrhythmogenic right ventricular dysplasia (ARVD) is a genetic cardiomyopathy characterized clinically by ventricular arrhythmias and progressive right ventricular (RV) dysfunction. The histopathologic hallmark is fibro-fatty replacement of RV myocardium. It is inherited in an autosomal pattern with variable penetrance. ARVD is unique in that it most commonly presents in young, otherwise health...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Journal of the American College of Cardiology
سال: 2017
ISSN: 0735-1097
DOI: 10.1016/s0735-1097(17)34864-7